Lung transplantation for cystic fibrosis – A complex nutritional setting

Abstract

Cystic fibrosis (CF) is an autosomal recessive, genetic disease that affects a variety of organs.^1,2 CF is caused by a mutation of chromosome 7 which results in defective control of sodium and chloride channels found in the cells that line a variety of organs.^1,2 This results in the production of a thick, sticky mucous that accumulates in the lungs and pancreatic ducts, as well as other mucous-producing organs.^1,2